While epispadias is inherent in all cases of exstrophy it can also, much less frequently, appear in isolation as the least severe form of the complex spectrum. Urgenciasquirurgicasurogenitales 479 asociacionespanoladepediatria. The exstrophyepispadias complex eec is the most serious form of abdominal midline malformation. Epispadias is an uncommon and partial form of a spectrum of failures of abdominal and pelvic fusion in the first months of embryogenesis known as the exstrophy epispadias complex. Introduction an epispadias is a rare type of malformation of the penis in which the urethra ends in an opening on the upper aspect the dorsum of the penis. Epidemioligy around 1 120,000 male 1500,000 female births. The abnormal opening can form anywhere from just below the end of the penis to the scrotum. May 03, 2017 epispadias is a rare birth defect in which the urethra, which is the opening, through which urine passes out of the body is not fully developed.
Roughly 90% of cases are the less serious distal hypospadias, in. Epispadias definicion defecto congenito del pene con orificio dorsal. Hypospadias is a congenital abnormality present since birth that occurs in about 1 in 250 newborn boys. Malformaciones congenitas del pene pdf free download. Prohibidalareproducciondeloscontenidossinlaautorizacioncorrespondiente. Hypospadias is the corresponding malformation in which the opening of the urethra is on the ventral surface underside of t. Episodial definition of episodial by the free dictionary. Urologia 18208a10 complejo extrofiaepispadias cee em consulte. Congenital at birth malformation in which the opening of the urethra from whence comes the urinary stream is on the dorsum topside of the penis. Hypospadias is a birth defect in boys in which the opening of the urethra is not located at the tip of the penis. Most cases involve more severe defects, including a small and bifid phallus with bladder exstrophy or even cloacal exstrophy involving the entire perineum.
Epispadia definition of epispadia by the free dictionary. All content on this website, including dictionary, thesaurus, literature, geography, and other reference data is for informational purposes only. The opening of the urethra is located away from the tip of the. Epispadias is a rare birth defect in which the urethra, which is the opening, through which urine passes out of the body is not fully developed. Our treatment was in the form of urethroplasty using cantwellyoung technique with satisfactory functional results. It is not strictly an inherited trait, like eye or hair colour, but it tends to occur more frequently in families where there is a history of hypospadias. Epispadias has been considered as the least severe defect of the exstrophyepispadias complex. In boys with hypospadias, the urethra forms abnormally during weeks 814 of pregnancy. Penile epispadias is a rare congenital urologic malformation. Since earlier descriptions the surgical management of the bladder exstrophy and epispadias complex. Know the causes, symptoms, treatment and types of epispadias. Hypospadias is a common variation in fetal development of the penis in which the urethra does not open from its usual location in the head of the penis. The bladder exstrophy is a serious anomaly of theurogenital. It can also develop in females when the urethra develops too far anteriorly 3.
We have performed these surgical procedure in 6 patients, 4 of them were epispadias a 23 years old patient who hado ther surgical procedure, with persistent incurvation, the others two. Caso clinico ana aliaga chueca eva antonaya rubia teresa bernues bergua c. Complejo extrofiaepispadias cee 030912 em consulte. It can also develop in females when the urethra develops too far anteriorly. An epispadias is a rare type of malformation of the penis in which the urethra ends in an opening on the upper aspect of the penis. Hipospadias mariel murillo morales summary hypospadias is a congenital abnormality of the male external genitalia relatively common. Epispadia synonyms, epispadia pronunciation, epispadia translation, english dictionary definition of epispadia. It is the secondmost common birth abnormality of the male reproductive system, affecting about one of every 250 males at birth. Tratamiento quirurgico del complejo extrofiaepispadias. An epispadias is an uncommon and partial form of a spectrum of failures of abdominal and pelvic fusion in the first months of embryogenesis. Malformazione congenita caratterizzata dallapertura delluretra alla parte superiore del pene nelluomo, della clitoride nella donna.
120 1508 213 659 232 1147 652 1504 1399 92 1142 1460 831 116 1292 1550 947 16 167 46 257 858 979 536 651 541 528